What Is A Gerst Mann Straussler Scheinker Syndrome?

March 22 20:41 2019 Print This Article

It is defined as a disorder in which there is a degeneration of the nerve. It is referred as the GSS. It is not a common condition and affects the people above the age of 20. It is a rare condition and is known as the transmissible spongiform encephalopathy and is known as TSE. The number of new cases of the disease is not known and is thought to be 1 per million. The familial cases are linked with the autosomal dominant.

What are the signs and symptoms of Gerst Mann straussler scheinker syndrome?

It includes the slow starting problem in the speaking as well as unsteadiness. It may lead to dementia in the later stages along with the loss of memory. There is a nerve problem which can lead to disease changes like the Alzheimer disease.

What are the causes of Gerst Mann straussler scheinker syndrome?

It includes the prions and there are small numbers of diseases. The prions are disease causing proteins which are not affected by the proteases. There is a change in the codon 102 from proline to leucine which is present on chromosome 20. So, mainly the genetic change is responsible for it.

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